ICD-11 classes
15 Diseases of the musculoskeletal system or connective...
Nonorgan specific systemic autoimmune disorders
4A44 — Vasculitis
4A44.A — Antineutrophil cytoplasmic antibody-associated vasculitis
4A44.A0 — Microscopic polyangiitis

ICD-11 4A44.A0 — Microscopic polyangiitis

Necrotizing vasculitis, with few or no immune deposits, predominantly affecting small vessels (i.e., capillaries, venules, or arterioles). Necrotizing arteritis involving small and medium sized arteries may be present. Necrotizing glomerulonephritis is very common. Pulmonary capillaritis often occurs. Granulomatous inflammation is absent.

It includes 1 item.

  • Microscopic polyarteritis

It excludes 1 item.

  • Polyarteritis nodosa (4A44.4)

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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