ICD-11 classes
15 Diseases of the musculoskeletal system or connective...
Nonorgan specific systemic autoimmune disorders
4A44 — Vasculitis
4A44.A — Antineutrophil cytoplasmic antibody-associated vasculitis
4A44.A1 — Granulomatosis with polyangiitis

ICD-11 4A44.A1 — Granulomatosis with polyangiitis

Necrotizing granulomatous inflammation usually involving the upper and lower respiratory tract, and necrotizing vasculitis affecting predominantly small to medium-sized vessels (e.g., capillaries, venules, arterioles, arteries and veins). Necrotizing glomerulonephritis is common . (Arthritis Rheum 1990; 33:1101-1107)

It includes 1 item.

  • Wegener granulomatosis

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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