ICD-11 classes
20 Developmental anomalies
Structural developmental anomalies primarily affecting one...
Structural developmental anomalies of the nervous system
LA04 — Congenital hydrocephalus
LA04.0 — Hydrocephalus with stenosis of the aqueduct of Sylvius
ICD-11 LA04.0 — Hydrocephalus with stenosis of the aqueduct of Sylvius
Hydrocephalus with stenosis of aqueduct of Sylvius (HSAS) or Bickers-Adams syndrome is characterised by the association of hydrocephaly, severe intellectual deficit, spasticity and adducted thumbs, and is part of the L1 syndrome (see this term).
It includes 1 item.
- Stenosis of the aqueduct of Sylvius
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: