ICD-11 classes
20 Developmental anomalies
Structural developmental anomalies primarily affecting one...
Structural developmental anomalies of the face, mouth or...
LA30 — Structural developmental anomalies of teeth and periodontal...
LA30.6 — Amelogenesis imperfecta
ICD-11 LA30.6 — Amelogenesis imperfecta
Amelogenesis imperfecta presents with a rare abnormal formation of the enamel or external layer of the crown of teeth. Amelogenesis imperfecta is due to the malfunction of the proteins in the enamel: ameloblastin, enamelin, tuftelin and amelogenin. People afflicted with amelogenesis imperfecta have teeth with abnormal colour: yellow, brown or grey; this disorder can afflict any number of teeth of both dentitions. The teeth have a higher risk for dental cavities and are hypersensitive to temperature changes as well as rapid attrition, excessive calculus deposition, and gingival hyperplasia.
It includes 2 items.
- Hypocalcified amelogenesis imperfecta
- Hypomaturation amelogenesis imperfecta
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: