ICD-11 classes
20 Developmental anomalies
Structural developmental anomalies primarily affecting one...
Structural developmental anomalies of the face, mouth or...
LA31 — Structural developmental anomalies of mouth or tongue
LA31.3 — Macrostomia

ICD-11 LA31.3 — Macrostomia

Congenital macrostomia or transverse facial cleft is a rare congenital craniofacial anomaly. It is usually associated with deformities of other structures developed from the first and second branchial arches and is thought to be part of the manifestations of hemifacial microsomia, the second most common congenital craniofacial anomaly.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Structural developmental anomalies of mouth or tongue #13473
• Structural developmental anomalies of mouth or tongue #16029