ICD-11 classes
01 Certain infectious or parasitic diseases
Certain staphylococcal or streptococcal diseases
Acute rheumatic fever

ICD-11 Acute rheumatic fever

A disease of the connective tissue, caused by an infection with the gram-positive bacteria Streptococcus pyogenes; (the disease may also affect the heart, joints, central nervous system, subcutaneous tissues, or skin). This disease is characterised by fever, polyarthritis, carditis, subcutaneous nodules, or erythema marginatum. Transmission is through haematogenous spread to other parts of the body after direct or indirect contact. Confirmation is by electrocardiography, sedimentation rate, or identification of Streptococcus pyogenes in a blood sample.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis contains 4 clarifying diagnoses:

1. 1B40 — Acute rheumatic fever without mention of heart involvement
   It contains 3 clarifying diagnoses.
2. 1B41 — Acute rheumatic fever with heart involvement
   It contains 5 clarifying diagnoses.
3. 1B42 — Rheumatic chorea
4. EA50.0 — Erythema marginatum rheumaticum