ICD-11 classes
01 Certain infectious or parasitic diseases
Certain staphylococcal or streptococcal diseases
Acute rheumatic fever
1B41 — Acute rheumatic fever with heart involvement

ICD-11 1B41 — Acute rheumatic fever with heart involvement

A disease of the cardiovascular system, caused as a result of rheumatic fever. Rheumatic heart disease is characterised by repeated inflammation with fibrinous repair. This disease may present with cardinal anatomic changes of the valve including leaflet thickening, commissural fusion, and shortening and thickening of the tendinous cords. Inflammation and valve scarring may also occur. Confirmation is by a thoracic radiography or echocardiography.

The diagnosis includes nothing.

It excludes 13 items.

  • Rheumatic mitral valve stenosis (BB60.0)
  • Rheumatic mitral valve insufficiency (BB61.0)
  • Rheumatic mitral valve prolapse (BB62.0)
  • Rheumatic mitral stenosis with insufficiency (BB63.0)
  • Rheumatic aortic valve stenosis (BB70.0)
  • Rheumatic aortic valve insufficiency (BB71.0)
  • Rheumatic aortic stenosis with insufficiency (BB72.0)
  • Rheumatic tricuspid valve stenosis (BB80.0)
  • Rheumatic tricuspid valve insufficiency (BB81.0)
  • Rheumatic tricuspid valve stenosis with insufficiency (BB82.0)
  • Rheumatic pulmonary valve stenosis (BB90.0)
  • Rheumatic pulmonary valve insufficiency (BB91.0)
  • Rheumatic pulmonary valve stenosis with insufficiency (BB92.0)

Diagnosis with code 1B41 contains 5 clarifying diagnoses:

  1. 1B41.0 — Acute rheumatic pericarditis
  2. 1B41.1 — Acute rheumatic endocarditis
    It contains 3 clarifying diagnoses.
  3. 1B41.2 — Acute rheumatic myocarditis
  4. 1B41.Y — Other acute rheumatic heart disease
  5. 1B41.Z — Acute rheumatic heart disease, unspecified

The diagnosis is coded elsewhere:

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