ICD-11 classes
03 Diseases of the blood or blood-forming organs
Neoplasms of haematopoietic or lymphoid tissues
Myeloproliferative neoplasms
2A21 — Mastocytosis
2A21.0 — Systemic mastocytosis
ICD-11 2A21.0 — Systemic mastocytosis
Systemic mastocytosis (SM) comprises a heterogeneous group of rare acquired and chronic haematological malignancies that are related to an abnormal proliferation of mast cells in tissue, including bone marrow, with or without skin involvement. SM can be divided into indolent SM (ISM) and aggressive SM (ASM).
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code 2A21.0 contains 3 clarifying diagnoses:
- 2A21.00 — Mast cell leukaemia
- 2A21.0Y — Other specified systemic mastocytosis
- 2A21.0Z — Systemic mastocytosis, unspecified
The diagnosis is coded elsewhere:
- Mastocytosis #1555
- Systemic mastocytosis #1556