ICD-11 classes
03 Diseases of the blood or blood-forming organs
Neoplasms of haematopoietic or lymphoid tissues
Mature B-cell neoplasms
2A84 — Heavy chain diseases or malignant immunoproliferative...
2A84.1 — Gamma heavy chain disease
ICD-11 2A84.1 — Gamma heavy chain disease
A clonal disorder characterised by the secretion of a truncated gamma chain. In most cases, it is associated with morphologic changes also seen in lymphoplasmacytic lymphomas, but the clinical course is typically more aggressive than in lymphoplasmacytic lymphoma/Waldenstrom's macroglobulinemia.
It includes 1 item.
- Franklin disease
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: