ICD-11 classes
03 Diseases of the blood or blood-forming organs
Neoplasms of haematopoietic or lymphoid tissues
Mature B-cell neoplasms
2A85 — Other specified mature B-cell neoplasms or lymphoma
2A85.4 — Lymphoplasmacytic lymphoma
ICD-11 2A85.4 — Lymphoplasmacytic lymphoma
Neoplasm of small B lymphocytes and plasma cells, mostly residing in the bone marrow. Frequently associated with the production of an IgM serum monoclonal protein, then called Waldenström macroglobulinemia (WM).
It includes 3 items.
- primary macroglobulinaemia
- Waldenström macroglobulinaemia
- Waldenström macroglobulinaemia without mention of remission
It excludes 2 items.
- small cell B-cell lymphoma (2A82.0)
- Chronic lymphocytic leukaemia or small lymphocytic lymphoma (2A82.0)
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: