ICD-11 classes
03 Diseases of the blood or blood-forming organs
Neoplasms of haematopoietic or lymphoid tissues
Mature T-cell or NK-cell neoplasms
2A90 — Mature T-cell lymphoma, specified types, nodal or systemic
2A90.4 — Systemic Epstein-Barr Virus-positive T-cell lymphoma of...
ICD-11 2A90.4 — Systemic Epstein-Barr Virus-positive T-cell lymphoma of childhood
This neoplasm of childhood is characterised by a clonal proliferation of EBV-infected T-cells with an activated cytotoxic phenotype. It can occur shortly after primary acute EBV infection or in the setting of chronic active EBV infection (CAEBV).
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: