ICD-11 classes
03 Diseases of the blood or blood-forming organs
Neoplasms of haematopoietic or lymphoid tissues
Mature T-cell or NK-cell neoplasms
2A90 — Mature T-cell lymphoma, specified types, nodal or systemic
2A90.A — Anaplastic large cell lymphoma, ALK-positive
ICD-11 2A90.A — Anaplastic large cell lymphoma, ALK-positive
A T-cell peripheral lymphoma composed of usually large, pleomorphic, CD30 positive T-lymphocytes with abundant cytoplasm characterised by the presence of a translocation involving the ALK gene and expression of ALK fusion protein. Most patients present with peripheral and/or abdominal lymphadenopathy, and often have advanced disease and extranodal involvement.
It includes 1 item.
- Anaplastic large cell lymphoma, CD30-positive
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: