ICD-11 classes
04 Diseases of the immune system
Primary immunodeficiencies
4A00 — Primary immunodeficiencies due to disorders of innate...

ICD-11 4A00 — Primary immunodeficiencies due to disorders of innate immunity

The diagnosis has no description.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 4A00 contains 7 clarifying diagnoses:

  1. 4A00.0 — Functional neutrophil defects
    It contains 4 clarifying diagnoses.
  2. 4A00.1 — Defects in the complement system
    It contains 8 clarifying diagnoses.
  3. 4A00.2 — Genetic susceptibility to particular pathogens
    It contains 2 clarifying diagnoses.
  4. 4A00.3 — Immunodeficiency with natural-killer cell deficiency
  5. 4B00.00 — Constitutional neutropaenia
  6. 4A00.Y — Other specified primary immunodeficiencies due to disorders of innate immunity
  7. 4A00.Z — Primary immunodeficiencies due to disorders of innate immunity, unspecified

The diagnosis is included in 1 another class.

  • Constitutional neutropaenia (4B00.00)

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