ICD-11 classes
04 Diseases of the immune system
Primary immunodeficiencies
4A00 — Primary immunodeficiencies due to disorders of innate...
4A00.1 — Defects in the complement system
ICD-11 4A00.1 — Defects in the complement system
The diagnosis has no description.
The diagnosis includes nothing.
It excludes 2 items.
- Atypical haemolytic uraemic syndrome (3A10)
- Paroxysmal nocturnal haemoglobinuria (3A21.0)
Diagnosis with code 4A00.1 contains 8 clarifying diagnoses:
- 4A00.10 — Immunodeficiency with an early component of complement deficiency
- 4A00.11 — Immunodeficiency with a late component of complement deficiency
- 4A00.12 — Immunodeficiency with factor B deficiency
- 4A00.13 — Immunodeficiency with factor D anomaly
- 4A00.14 — Hereditary angioedema
- 4A00.15 — Acquired angioedema
- 4A00.1Y — Other specified defects in the complement system
- 4A00.1Z — Defects in the complement system, unspecified
The diagnosis is coded elsewhere: