ICD-11 classes
04 Diseases of the immune system
Immune system disorders involving white cell lineages
4A00.1 — Defects in the complement system

ICD-11 4A00.1 — Defects in the complement system

The diagnosis has no description.

The diagnosis includes nothing.

Diagnosis with code 4A00.1 contains 8 clarifying diagnoses:

1. 4A00.10 — Immunodeficiency with an early component of complement deficiency
2. 4A00.11 — Immunodeficiency with a late component of complement deficiency
3. 4A00.12 — Immunodeficiency with factor B deficiency
4. 4A00.13 — Immunodeficiency with factor D anomaly
5. 4A00.14 — Hereditary angioedema
6. 4A00.15 — Acquired angioedema
7. 4A00.1Y — Other specified defects in the complement system
8. 4A00.1Z — Defects in the complement system, unspecified

The diagnosis is coded elsewhere:

• Primary immunodeficiencies due to disorders of innate immunity #3521
• Defects in the complement system #3527