ICD-11 classes
04 Diseases of the immune system
Immune system disorders involving white cell lineages
4A00.1 — Defects in the complement system
4A00.13 — Immunodeficiency with factor D anomaly

ICD-11 4A00.13 — Immunodeficiency with factor D anomaly

Factor D deficiency is an autosomal recessive immunologic disorder characterised by increased susceptibility to bacterial infections, particularly Neisseria infections, due to a defect in the alternative complement pathway.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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