ICD-11 classes
04 Diseases of the immune system
Primary immunodeficiencies
4A01 — Primary immunodeficiencies due to disorders of adaptive...
4A01.0 — Immunodeficiencies with predominantly antibody defects
4A01.00 — Hereditary agammaglobulinaemia with profoundly reduced or...
ICD-11 4A01.00 — Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
This refers to a hereditary type of primary immune deficiency disease characterised by a reduction in all types of gamma globulins, and rare X-linked genetic disorder that affects the body's ability to fight infection.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: