ICD-11 classes
04 Diseases of the immune system
Primary immunodeficiencies
4A01 — Primary immunodeficiencies due to disorders of adaptive...
4A01.0 — Immunodeficiencies with predominantly antibody defects

ICD-11 4A01.0 — Immunodeficiencies with predominantly antibody defects

A disorder characterised by an inability to mount a normal immune response due to antibody (i.e. immunoglobulin) defects

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 4A01.0 contains 8 clarifying diagnoses:

1. 4A01.00 — Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
2. 4A01.01 — Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells
3. 4A01.02 — Specific antibody deficiency with normal immunoglobulin concentrations or normal number of B cells
4. 4A01.03 — Transient hypogammaglobulinaemia of infancy
5. 4A01.04 — Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells
6. 4A01.05 — Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells
7. 4A01.0Y — Other specified immunodeficiencies with predominantly antibody defects
8. 4A01.0Z — Immunodeficiencies with predominantly antibody defects, unspecified

The diagnosis is coded elsewhere:

• Immune system disorders involving white cell lineages #3963
• Immunodeficiencies with predominantly antibody defects #4008