ICD-11 classes
04 Diseases of the immune system
Primary immunodeficiencies
4A01 — Primary immunodeficiencies due to disorders of adaptive...
4A01.0 — Immunodeficiencies with predominantly antibody defects
4A01.05 — Immunodeficiencies with severe reduction in serum IgG or...

ICD-11 4A01.05 — Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells

The diagnosis has no description.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

The diagnosis is included in 2 other classes.

  • Hyper-IgM syndrome due to CD40 ligand deficiency (4A01.1Y)
  • Hyper-IgM syndrome due to CD40 deficiency (4A01.1Y)

Search results