ICD-11 classes
04 Diseases of the immune system
Primary immunodeficiencies
4A01 — Primary immunodeficiencies due to disorders of adaptive...
4A01.3 — Other well-defined immunodeficiency syndromes due to...

ICD-11 4A01.3 — Other well-defined immunodeficiency syndromes due to defects in adaptive immunity

This refers to other defects in the highly specialized, systemic cells and processes that eliminate or prevent pathogen growth.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 4A01.3 contains 5 clarifying diagnoses:

1. 4A01.30 — Immunodeficiency due to defects of the thymus
   It contains 1 clarifying diagnosis.
2. 4A01.31 — DNA repair defects other than combined T-cell or B-cell immunodeficiencies
3. 4A01.32 — Immuno-osseous dysplasia
4. 4A01.33 — Hepatic veno-occlusive disease - immunodeficiency syndrome
5. 4A01.34 — Hyperimmunoglobulin E syndromes

The diagnosis is coded elsewhere:

• Immune system disorders involving white cell lineages #3963