ICD-11 classes
04 Diseases of the immune system
Primary immunodeficiencies
4A01 — Primary immunodeficiencies due to disorders of adaptive...
4A01.3 — Other well-defined immunodeficiency syndromes due to...
4A01.33 — Hepatic veno-occlusive disease - immunodeficiency syndrome

ICD-11 4A01.33 — Hepatic veno-occlusive disease - immunodeficiency syndrome

Hepatic veno-occlusive disease — immunodeficiency syndrome is characterised by the association of severe hypogammaglobulinemia, combined T and B cell immunodeficiency, absent lymph node germinal centres, absent tissue plasma cells and hepatic veno-occlusive disease.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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