ICD-11 classes
04 Diseases of the immune system
Nonorgan specific systemic autoimmune disorders
4A40 — Lupus erythematosus
ICD-11 4A40 — Lupus erythematosus
An autoimmune non-organ specific inflammatory disease characterised by the presence of antibodies to DNA, RNA and other components of the nucleus. It has a very variable clinical presentation and course ranging from an acute fulminant life-threatening disorder with involvement of heart, central nervous system and kidneys to an indolent chronic scarring skin disorder.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code 4A40 contains 7 clarifying diagnoses:
- 4A40.0 — Systemic lupus erythematosus
It contains 3 clarifying diagnoses. - 4A40.1 — Drug-induced lupus erythematosus
- EB50 — Subacute cutaneous lupus erythematosus
- EB51 — Chronic cutaneous lupus erythematosus
It contains 2 clarifying diagnoses. - KA07.0 — Neonatal lupus erythematosus
- 4A40.Y — Other specified lupus erythematosus
- 4A40.Z — Lupus erythematosus, unspecified
The diagnosis is coded elsewhere:
The diagnosis is included in 3 other classes.
- Subacute cutaneous lupus erythematosus (EB50)
- Chronic cutaneous lupus erythematosus (EB51)
- Neonatal lupus erythematosus (KA07.0)