ICD-11 classes
04 Diseases of the immune system
Nonorgan specific systemic autoimmune disorders
4A40 — Lupus erythematosus
EB51 — Chronic cutaneous lupus erythematosus
ICD-11 EB51 — Chronic cutaneous lupus erythematosus
Chronic cutaneous lupus erythematosus (LE) is characterised by the presence of circumscribed cutaneous plaques showing varying degrees of oedema, erythema, scaling, follicular plugging and atrophy. It most commonly presents as discoid plaques involving the face, ears and scalp but can be widely disseminated or may affect predominantly the extremities (chilblain LE) or subcutaneous fat (lupus panniculitis). It can cause marked disfigurement with prominent facial scarring and permanent hair loss. Most patients remain otherwise in good health but 5-10% may develop systemic lupus erythematosus. Photosensitivity is less apparent than in subacute cutaneous lupus erythematosus.
The diagnosis includes nothing.
It excludes 1 item.
- Systemic lupus erythematosus (4A40.0)
Diagnosis with code EB51 contains 2 clarifying diagnoses:
The diagnosis is coded elsewhere:
- Cutaneous lupus erythematosus #15806
- Chronic cutaneous lupus erythematosus #15808
- Cutaneous lupus erythematosus #17249
- Chronic cutaneous lupus erythematosus #17251
- Lupus erythematosus #18346
- Chronic cutaneous lupus erythematosus #18353