ICD-11 classes
04 Diseases of the immune system
Nonorgan specific systemic autoimmune disorders
4A41 — Idiopathic inflammatory myopathy
4A41.2 — Inclusion body myopathy
4A41.21 — Noninflammatory inclusion body myopathy
ICD-11 4A41.21 — Noninflammatory inclusion body myopathy
Noninflammatory inclusion body myopathy (IBM) is an idiopathic muscle disorder without inflammatory exudates and expression of class I major histocompatibility complex. Rimmed vacuoles and “IBM-like” filaments without inflammatory cells are described in muscle biopsy.
The diagnosis includes nothing.
It excludes 1 item.
- Myasthenia gravis or certain specified neuromuscular junction disorders (8C60-8C6Z)
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Inclusion body myopathy #7515
- Inclusion body myopathy #10083
- Inclusion body myopathy #18369