ICD-11 classes
04 Diseases of the immune system
Immune system disorders involving white cell lineages
4B01 — Disorders of neutrophil function
4A00.0 — Functional neutrophil defects

ICD-11 4A00.0 — Functional neutrophil defects

The diagnosis has no description.

It includes 1 item.

  • Congenital dysphagocytosis

The diagnosis excludes nothing.

Diagnosis with code 4A00.0 contains 4 clarifying diagnoses:

  1. 4A00.00 — Neutrophil immunodeficiency syndrome
  2. 3A10.00 — Haemolytic anaemia due to glucose-6-phosphate dehydrogenase deficiency
  3. 4A00.0Y — Other specified functional neutrophil defects
  4. 4A00.0Z — Functional neutrophil defects, unspecified

The diagnosis is coded elsewhere:

The diagnosis is included in 2 other classes.

  • Haemolytic anaemia due to glucose-6-phosphate dehydrogenase deficiency (3A10.00)
  • Papillon-Lefèvre syndrome (EC20.30)

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