ICD-11 classes
04 Diseases of the immune system
Immune system disorders involving white cell lineages
4A01.1 — Combined immunodeficiencies

ICD-11 4A01.1 — Combined immunodeficiencies

The diagnosis has no description.

The diagnosis includes nothing.

It excludes 1 item.

  • autosomal recessive agammaglobulinaemia (Swiss type) (4A01.00)

Diagnosis with code 4A01.1 contains 5 clarifying diagnoses:

  1. 4A01.10 — Severe combined immunodeficiencies
  2. 4A01.11 — Major histocompatibility complex class I deficiency
  3. 4A01.12 — Major histocompatibility complex class II deficiency
  4. 4A01.1Y — Other specified combined immunodeficiencies
  5. 4A01.1Z — Combined immunodeficiencies, unspecified

The diagnosis is coded elsewhere:

The diagnosis is included in 1 another class.

  • Laron syndrome with immunodeficiency (5A61.0)

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