ICD-11 classes
04 Diseases of the immune system
Immune system disorders involving white cell lineages
4A01.1 — Combined immunodeficiencies
4A01.10 — Severe combined immunodeficiencies

ICD-11 4A01.10 — Severe combined immunodeficiencies

Severe combined immunodeficiency (SCID) comprises a group of rare monogenic primary immunodeficiency disorders characterised by a lack of functional peripheral T lymphocytes resulting in early-onset severe respiratory infections and failure to thrive.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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