ICD-11 classes
04 Diseases of the immune system
Immune system disorders involving white cell lineages
4A01.2 — Diseases of immune dysregulation
4A01.21 — Immune dysregulation syndromes presenting primarily with...
ICD-11 4A01.21 — Immune dysregulation syndromes presenting primarily with autoimmunity
The diagnosis has no description.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
The diagnosis is included in 4 other classes.
- Autoimmune polyendocrinopathy type 1 (5B00)
- Syndromic multisystem autoimmune disease due to ITCH deficiency (4A43.Y)
- Aicardi-Goutières syndrome (5C55.2)
- Spondylometaphyseal dysplasia with combined immunodeficiency (LD24.4)