ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C50 — Inborn errors of amino acid or other organic acid metabolism
5C50.E — Organic aciduria
ICD-11 5C50.E — Organic aciduria
An inborn error of metabolism disrupting normal amino acid metabolism, particularly branched-chain amino acids, causing a buildup of acids, which are usually not present
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code 5C50.E contains 4 clarifying diagnoses:
- 5C50.E0 — Classical organic aciduria
- 5C50.E1 — Cerebral organic aciduria
- 5C50.EY — Other specified organic aciduria
- 5C50.EZ — Organic aciduria, unspecified