ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C50 — Inborn errors of amino acid or other organic acid metabolism
5C50.E — Organic aciduria
5C50.E0 — Classical organic aciduria

ICD-11 5C50.E0 — Classical organic aciduria

This a term used to classify a group of metabolic disorders which disrupt normal amino acid metabolism, particularly branched-chain amino acids, causing a buildup of acids which are usually not present.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is included in 1 another class.

  • Ketoacidosis due to beta-ketothiolase deficiency (5C50.DY)

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