ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C51 — Inborn errors of carbohydrate metabolism

ICD-11 5C51 — Inborn errors of carbohydrate metabolism

The diagnosis has no description.

The diagnosis includes nothing.

It excludes 4 items.

  • Increased secretion of glucagon (5A42)
  • Diabetes mellitus (5A10-5A2Y)
  • hypoglycaemia NOS (5A41)
  • Mucopolysaccharidosis (5C56.3)

Diagnosis with code 5C51 contains 9 clarifying diagnoses:

  1. 5C51.0 — Disorders of the pentose phosphate pathway
    It contains 1 clarifying diagnosis.
  2. 5C51.1 — Disorders of glycerol metabolism
  3. 5C51.2 — Disorders of glyoxylate metabolism
    It contains 3 clarifying diagnoses.
  4. 5C51.3 — Glycogen storage disease
  5. 5C51.4 — Disorders of galactose metabolism
    It contains 5 clarifying diagnoses.
  6. 5C51.5 — Disorders of fructose metabolism
    It contains 4 clarifying diagnoses.
  7. KB60 — Transitory disorders of carbohydrate metabolism specific to fetus or newborn
    It contains 7 clarifying diagnoses.
  8. 5C51.Y — Other specified inborn errors of carbohydrate metabolism
  9. 5C51.Z — Inborn errors of carbohydrate metabolism, unspecified

The diagnosis is included in 1 another class.

  • Transitory disorders of carbohydrate metabolism specific to fetus or newborn (KB60)

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