ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C51 — Inborn errors of carbohydrate metabolism
5C51.5 — Disorders of fructose metabolism
ICD-11 5C51.5 — Disorders of fructose metabolism
This refers to disorders of the metabolism of fructose in the phosphorylation of fructose to fructose 1-phosphate by fructokinase, thus trapping fructose for metabolism in the liver.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code 5C51.5 contains 4 clarifying diagnoses:
- 5C51.50 — Hereditary fructose intolerance
- 5C61.40 — Fructose malabsorption
- 5C51.5Y — Other specified disorders of fructose metabolism
- 5C51.5Z — Disorders of fructose metabolism, unspecified
The diagnosis is coded elsewhere:
- Metabolic or transporter liver disease #5084
- Disorders of fructose metabolism #5118
- Metabolic or transporter liver disease #14401
- Disorders of fructose metabolism #14435
The diagnosis is included in 1 another class.
- Fructose malabsorption (5C61.40)