ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
5C90 — Metabolic or transporter liver disease
5C51.5 — Disorders of fructose metabolism

ICD-11 5C51.5 — Disorders of fructose metabolism

This refers to disorders of the metabolism of fructose in the phosphorylation of fructose to fructose 1-phosphate by fructokinase, thus trapping fructose for metabolism in the liver.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 5C51.5 contains 4 clarifying diagnoses:

  1. 5C51.50 — Hereditary fructose intolerance
  2. 5C61.40 — Fructose malabsorption
  3. 5C51.5Y — Other specified disorders of fructose metabolism
  4. 5C51.5Z — Disorders of fructose metabolism, unspecified

The diagnosis is coded elsewhere:

The diagnosis is included in 1 another class.

  • Fructose malabsorption (5C61.40)

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