ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C53 — Inborn errors of energy metabolism
5C53.0 — Disorders of pyruvate metabolism

ICD-11 5C53.0 — Disorders of pyruvate metabolism

The diagnosis has no description.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 5C53.0 contains 6 clarifying diagnoses:

  1. 5C53.00 — Pyruvate kinase deficiency
  2. 5C53.01 — Lactate dehydrogenase deficiency
  3. 5C53.02 — Pyruvate dehydrogenase complex deficiency
  4. 5C53.03 — Pyruvate carboxylase deficiency
  5. 5C53.0Y — Other specified disorders of pyruvate metabolism
  6. 5C53.0Z — Disorders of pyruvate metabolism, unspecified

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