ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C53 — Inborn errors of energy metabolism

ICD-11 5C53 — Inborn errors of energy metabolism

The diagnosis has no description.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 5C53 contains 7 clarifying diagnoses:

  1. 5C53.0 — Disorders of pyruvate metabolism
    It contains 6 clarifying diagnoses.
  2. 5C53.1 — Disorders of the citric acid cycle
  3. 5C53.2 — Disorders of mitochondrial oxidative phosphorylation
    It contains 9 clarifying diagnoses.
  4. 5C53.3 — Disorders of mitochondrial membrane transport
    It contains 4 clarifying diagnoses.
  5. 5C53.4 — Disorders of creatine metabolism
  6. 5C53.Y — Other specified inborn errors of energy metabolism
  7. 5C53.Z — Inborn errors of energy metabolism, unspecified

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