ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C53 — Inborn errors of energy metabolism
5C53.3 — Disorders of mitochondrial membrane transport

ICD-11 5C53.3 — Disorders of mitochondrial membrane transport

An inborn error of metabolism in proteins in the membranes of mitochondria, which serve to transport molecules and other factors such as ions into or out of the organelles

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 5C53.3 contains 4 clarifying diagnoses:

1. 5C53.30 — Mitochondrial substrate carrier disorders
2. 5C53.31 — Mitochondrial protein import disorders
3. 5C53.3Y — Other specified disorders of mitochondrial membrane transport
4. 5C53.3Z — Disorders of mitochondrial membrane transport, unspecified