ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C53 — Inborn errors of energy metabolism
5C53.2 — Disorders of mitochondrial oxidative phosphorylation
5C53.22 — Coenzyme Q10 deficiency

ICD-11 5C53.22 — Coenzyme Q10 deficiency

This is a deficiency in a 1,4-benzoquinone, where Q refers to the quinone chemical group, and 10 refers to the number of isoprenyl chemical subunits in its tail. This oil-soluble, vitamin-like substance is present in most eukaryotic cells, primarily in the mitochondria. It is a component of the electron transport chain and participates in aerobic cellular respiration, generating energy in the form of ATP.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.