ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C56 — Lysosomal diseases
5C56.0 — Sphingolipidosis

ICD-11 5C56.0 — Sphingolipidosis

The diagnosis has no description.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 5C56.0 contains 6 clarifying diagnoses:

  1. 5C56.00 — Gangliosidosis
  2. 5C56.01 — Fabry disease
  3. 5C56.02 — Metachromatic leukodystrophy
  4. 8A44.4 — Krabbe disease
  5. 5C56.0Y — Other specified sphingolipidosis
  6. 5C56.0Z — Sphingolipidosis, unspecified

The diagnosis is included in 1 another class.

  • Krabbe disease (8A44.4)

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