ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C56 — Lysosomal diseases

ICD-11 5C56 — Lysosomal diseases

The diagnosis has no description.

The diagnosis includes nothing.

It excludes 1 item.

  • Glycogen storage disease due to LAMP-2 deficiency (5C51.3)

Diagnosis with code 5C56 contains 7 clarifying diagnoses:

  1. 5C56.0 — Sphingolipidosis
    It contains 6 clarifying diagnoses.
  2. 5C56.1 — Neuronal ceroid lipofuscinosis
  3. 5C56.2 — Glycoproteinosis
    It contains 4 clarifying diagnoses.
  4. 5C56.3 — Mucopolysaccharidosis
    It contains 6 clarifying diagnoses.
  5. 5C56.4 — Disorders of sialic acid metabolism
  6. 5C56.Y — Other specified lysosomal diseases
  7. 5C56.Z — Lysosomal diseases, unspecified

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