ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C56 — Lysosomal diseases
5C56.2 — Glycoproteinosis

ICD-11 5C56.2 — Glycoproteinosis

These are lysosomal storage diseases affecting glycoproteins, resulting from defects in lysosomal function. The term is sometimes reserved for conditions involving degradation of glycoproteins.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 5C56.2 contains 4 clarifying diagnoses:

  1. 5C56.20 — Mucolipidosis
  2. 5C56.21 — Oligosaccharidosis
  3. 5C56.2Y — Other specified glycoproteinosis
  4. 5C56.2Z — Glycoproteinosis, unspecified

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