ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C56 — Lysosomal diseases
5C56.3 — Mucopolysaccharidosis

ICD-11 5C56.3 — Mucopolysaccharidosis

The diagnosis has no description.

It includes 1 item.

  • Disorders of glycosaminoglycan metabolism

The diagnosis excludes nothing.

Diagnosis with code 5C56.3 contains 6 clarifying diagnoses:

  1. 5C56.30 — Mucopolysaccharidosis type 1
  2. 5C56.31 — Mucopolysaccharidosis type 2
  3. 5C56.32 — Mucopolysaccharidosis type 4
  4. 5C56.33 — Mucopolysaccharidosis type 6
  5. 5C56.3Y — Other specified mucopolysaccharidosis
  6. 5C56.3Z — Mucopolysaccharidosis, unspecified

The diagnosis is coded elsewhere:

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