ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Inborn errors of metabolism
5C58 — Inborn errors of porphyrin or heme metabolism
5C58.1 — Porphyrias
5C58.13 — Variegate porphyria
ICD-11 5C58.13 — Variegate porphyria
Variegate porphyria is a form of acute hepatic porphyria characterised by the occurrence of neuro-visceral attacks with or without the presence of cutaneous lesions (bullous photodermatitis).
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Liver diseases due to disorders of porphyrin or bilirubin metabolism or transport #5089
- Liver diseases due to disorders of porphyrin or bilirubin metabolism or transport #14406
- Porphyria or pseudoporphyria affecting the skin #15894
- Genetic and developmental disorders affecting the skin #15936
- Porphyria or pseudoporphyria affecting the skin #17243