ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
5C90 — Metabolic or transporter liver disease
5C90.0 — Liver diseases due to urea cycle defects
ICD-11 5C90.0 — Liver diseases due to urea cycle defects
This is a group of liver diseases due to defects in the urea cycle, which is a metabolic cycle of nitrogen-containing compounds that produces the waste product urea.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code 5C90.0 contains 3 clarifying diagnoses:
- 5C50.A0 — Argininosuccinic aciduria
- 5C50.A1 — Carbamoylphosphate synthetase deficiency
- 5C50.A2 — Argininaemia
The diagnosis is coded elsewhere:
The diagnosis is included in 4 other classes.
- Argininosuccinic aciduria (5C50.A0)
- Carbamoylphosphate synthetase deficiency (5C50.A1)
- Argininaemia (5C50.A2)
- Ornithine carbamoyltransferase deficiency (5C50.AY)