ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
5C90 — Metabolic or transporter liver disease
5C90.2 — Liver diseases due to disorders of amino acid metabolism
5C50.1 — Disorders of tyrosine metabolism

ICD-11 5C50.1 — Disorders of tyrosine metabolism

The diagnosis has no description.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 5C50.1 contains 6 clarifying diagnoses:

  1. 5C50.10 — Alkaptonuria
  2. 5C50.11 — Tyrosinaemia type 1
  3. 5C50.12 — Tyrosinaemia type 2
  4. KB63.4 — Transitory tyrosinaemia of newborn
  5. 5C50.1Y — Other specified disorders of tyrosine metabolism
  6. 5C50.1Z — Disorders of tyrosine metabolism, unspecified

The diagnosis is coded elsewhere:

The diagnosis is included in 4 other classes.

  • Transitory tyrosinaemia of newborn (KB63.4)
  • Autosomal recessive dopa-responsive dystonia (8A02.11)
  • Oculocutaneous albinism type 1A (EC23.20)
  • Oculocutaneous albinism type 1B (EC23.20)

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