ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
5C90 — Metabolic or transporter liver disease
5C90.2 — Liver diseases due to disorders of amino acid metabolism

ICD-11 5C90.2 — Liver diseases due to disorders of amino acid metabolism

This is liver disease due to the disorder of the various biochemical processes responsible for the synthesis of proteins and amino acids, and the breakdown of proteins (and other large molecules, too) by catabolism.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 5C90.2 contains 2 clarifying diagnoses:

  1. 5C50.1 — Disorders of tyrosine metabolism
    It contains 6 clarifying diagnoses.
  2. 5C50.A3 — Citrullinaemia

The diagnosis is coded elsewhere:

The diagnosis is included in 2 other classes.

  • Disorders of tyrosine metabolism (5C50.1)
  • Citrullinaemia (5C50.A3)

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