ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Other metabolic disorders
5D00 — Amyloidosis

ICD-11 5D00 — Amyloidosis

Amyloidosis is a vast group of diseases defined by the presence of insoluble protein deposits in tissues. Its diagnosis is based on histological findings. Amyloidoses are classified according to clinical signs and biochemical type of amyloid protein involved. Most amyloidoses are multisystemic, 'generalised' or 'diffuse'. There are a few forms of localised amylosis. The most frequent forms are AL amyloidosis (immunoglobulins), AA (inflammatory), and ATTR (transthyretin accumulation).

The diagnosis includes nothing.

Diagnosis with code 5D00 contains 6 clarifying diagnoses:

1. 5D00.0 — AL amyloidosis
   It contains 1 clarifying diagnosis.
2. 5D00.1 — AA amyloidosis
3. 5D00.2 — Hereditary amyloidosis
   It contains 4 clarifying diagnoses.
4. 5D00.3 — Dialysis-associated amyloidosis
5. 5D00.Y — Other specified amyloidosis
6. 5D00.Z — Amyloidosis, unspecified