ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Other metabolic disorders
5D00 — Amyloidosis
5D00.0 — AL amyloidosis
ICD-11 5D00.0 — AL amyloidosis
AL amyloid is due to the deposition of immunoglobulin light chains in glomeruli where they are seen as Congo red binding fibrils and immuno-stain specifically for kappa or lambda light chains. By light microscopy there is amorphous hyaline material in the mesangium and capillary walls. A light chain producing plasma cell or B-cell dysplasia is responsible. Other organs are also involved in this systemic disease.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code 5D00.0 contains 1 clarifying diagnosis:
- 8B22.3 — Isolated cerebral amyloid angiopathy
The diagnosis is included in 1 another class.
- Isolated cerebral amyloid angiopathy (8B22.3)