ICD-11 classes
05 Endocrine, nutritional or metabolic diseases
Metabolic disorders
Other metabolic disorders
5D00 — Amyloidosis
5D00.2 — Hereditary amyloidosis
5D00.21 — Non-neuropathic heredofamilial amyloidosis
ICD-11 5D00.21 — Non-neuropathic heredofamilial amyloidosis
This is an amyloidosis (the formation of insoluble proteins, or amyloids) of inherited origin that does not affect the peripheral nerves. The most common sites of deposits are associated with the kidney and heart.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is included in 1 another class.
- Familial Mediterranean fever with amyloidosis (4A60.0)