ICD-11 classes
08 Diseases of the nervous system
Multiple sclerosis or other white matter disorders
8A44 — Leukodystrophies
5C56.02 — Metachromatic leukodystrophy
ICD-11 5C56.02 — Metachromatic leukodystrophy
Metachromatic leukodystrophy is a neurodegenerative disease characterised by an accumulation of sulfatides (sulphated glycosphingolipids, especially sulfogalactosylceramides or sulfogalactocerebrosides) in the nervous system and kidneys. Three forms of the disease exist: late infantile, juvenile and adult.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: