ICD-11 classes
08 Diseases of the nervous system
Epilepsy or seizures
8A61 — Genetic or presumed genetic syndromes primarily expressed...
8A61.1 — Genetic epileptic syndromes with onset in infancy

ICD-11 8A61.1 — Genetic epileptic syndromes with onset in infancy

Include a vast spectrum of phenotypes having in common a genetic background and the onset in infancy. They range from benign self-remitting to severe drug resistant syndromes. Family history of epilepsy is common in some syndromic entities and exceptional in others.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 8A61.1 contains 5 clarifying diagnoses:

1. 8A61.10 — Benign familial infantile epilepsy
2. 8A61.11 — Dravet syndrome
3. 8A61.12 — Epilepsy of infancy with migrating focal seizures
4. 8A61.1Y — Other specified genetic epileptic syndromes with onset in infancy
5. 8A61.1Z — Genetic epileptic syndromes with onset in infancy, unspecified